Report of a Rare Case of Epitheliod Hemangioendothelioma in Tongue

Bajpai, Manas; Pardhe, Nilesh

doi:10.30476/dentjods.2019.44567

Document Type : Case Report

Authors

Dept. of Oral and Maxillofacial Pathology, NIMS Dental College, Jaipur, India.

https://doi.org/10.30476/dentjods.2019.44567

Abstract

Epitheloid hemangioendothelioma (EHE) is a rare vascular neoplasm of intermediate malignant potential. EHE commonly involves lungs, liver soft tissue, and bone. EHE is extremely rare in tongue and up to our best knowledge only nine cases of EHE of tongue reported in the literature. Clinically EHE usually presents as an asymptomatic mass. Microscopically, EHE exhibits proliferation of epitheloid cells and spindle shaped endothelial cells. Epitheloid cells show cytoplasmic vacuoles with few cells containing RBCs. A 34-year-old male presented to our institution with the chief complain of swelling on the base of the tongue from eight months. Surgical excision was done. An extensive work up of immunohistochemistry was done using different markers including CD 31, CD 34, Ki 67, Factor VIII, and BCL2. Correlation of histopathology and immunohistochemistry confirmed the diagnosis of EHE. The follow up period of 2 years was uneventful.

Keywords

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Journal of Dentistry

Report of a Rare Case of Epitheliod Hemangioendothelioma in Tongue

References

References

Volume 20, Issue 1 - Serial Number 1
March 2019
Pages 70-74

Report of a Rare Case of Epitheliod Hemangioendothelioma in Tongue

References

References

Volume 20, Issue 1 - Serial Number 1March 2019Pages 70-74

Volume 20, Issue 1 - Serial Number 1
March 2019
Pages 70-74