Document Type: Case Report

Authors

1 Dept. of Pediatric Dentistry, Islamic Azad University, Dental Branch, Tehran, Iran.

2 Mofid’s Children Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.

3 Dept. of Pediatric Dentistry, School of Dentistry, Shahid Beheshti University of Medical Sciences, Tehran, Iran.

4 Instructor of Child Neurology and Neurodevelopmental Disabilities. UMDNJ/ Robert Wood Johnson Medical School, NJ, USA.

Abstract

Epidermolysis bullosa (EB) is a group of rare inherited skin and mucous membrane disorders in which blister formation may arise spontaneously or following a minor friction. Various patterns of inheritance are explicated for the disease. The disease has a profound effect on oral mucosa and may result in high prevalence of dental caries. General anesthesia is sometimes the only choice for dental treatments in patients with EB. The following case report describes the dental and anesthetic management of an 12.5 -year-old girl with dystrophic type of EB. The patient was followed up every 6 months. New carious lesions were detected one year after the treatment, on the last visit. Presenting a perfect dental care to children with this disorder can be challenging for the in charge specialist, both pediatric dentist and anesthesiologist.