Document Type : Case Report
Authors
1 Dept. of Oral and Maxillofacial Pathology, Post Graduate Institute of Dental Sciences, Rohtak, Haryana, India.
2 Dr. R. Ahmed Dental College & Hospital, Kolkata, India.
Abstract
Segmental odontomaxillary dysplasia is a rare developmental anomaly of the maxilla, typically diagnosed in early childhood. It is characterized by unilateral buccolingual expansion of the posterior alveolar process, gingival enlargement, and delayed eruption of adjacent teeth, and dental anomalies such as malformed primary molars and absence of premolars in the affected region. Several cases exhibit homolateral cutaneous manifestations, including facial scars or hyperpigmented patches. Radiographically, the affected bone shows thickened and irregular, with a coarse, vertically oriented trabecular pattern, producing a radiopaque granular appearance. A brief systematic review of previously reported cases was conducted to analyze demographic characteristics, clinical presentation, radiographic features, and management strategies. Based on the literature and current findings, a diagnostic algorithm was developed to facilitate differentiation from similar unilateral maxillary conditions. Herein, we report the case of a 5-year-old girl who presented with mild facial asymmetry and a hyperpigmented scar over the mid-cheek region and gingival overgrowth in the left posterior maxilla.
Keywords
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